A SUCCESSFUL CASE OF THORACOABDOMINAL AORTIC ANEURYSM TYPE 3 RESECTION AFTER THE RECONSTRUCTION OF THE WHOLE THORACIC AORTA

In young people thoracoabdominal aortic aneurysms are more often connected with pathology of connective tissue. The main problem is choosing between the minimally invasive endovascular surgery and open surgery of thoracoabdominal aortic aneurysm. The development of endovascular approaches to thoracoabdominal aortic aneurysm has led to the fact that they are becoming more and more attractive method of treatment, compared with open aortic reconstruction due to lower operational mortality and complications of the internal organs and spinal cord. However, the percentage of surgical interventions after endovascular treatment of thoracoabdominal aneurysms range from 0.4 to 7.9% according to the statistics of different clinics. Patients with connective tissue pathology after endovascular interventions have a high risk of aortic dilatation progressing. According to the latest data from domestic and foreign studies, open surgical treatment may be more suitable for young patients (under 50 years). A group of young patients with open surgery had more thoracoabdominal aneurysms type 2, longer aortic clamping time, a greater percentage of visceral artery reconstructions. However, open surgical treatment has lower operational mortality, persistent neurological disorders, renal disorders requiring dialysis, compared with a group of patients older than 50 years. This clinical case illustrates a successful prosthetics of the whole aorta for connective tissue disease at a young age. Keywords: connective tissue disorders; thoracoabdominal aortic aneurysm; total aortic replacement.

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